About Isobutyryl-CoA Dehydrogenase Deficiency

Isobutyryl-Coa Dehydrogenase Deficiency, also known as ibd deficiency, is related to acyl-coa dehydrogenase, short-chain, deficiency of and dilated cardiomyopathy. An important gene associated with Isobutyryl-Coa Dehydrogenase Deficiency is ACAD8 (Acyl-CoA Dehydrogenase Family Member 8). Affiliated tissues include heart, and related phenotypes are decreased plasma carnitine and dicarboxylic aciduria

Major Symptoms of Isobutyryl-CoA Dehydrogenase Deficiency

Isobutyryl-CoA dehydrogenase (IBD) deficiency is a rare genetic disorder characterized by the inability to produce Isobutyryl-CoA (IBC) in the body, which is a key step in the citric acid cycle. The major symptoms of IBD deficiency include:

Suitable Lifestyle for People with Isobutyryl-CoA Dehydrogenase Deficiency

Isobutyryl-CoA dehydrogenase (Ischemic in Hand) deficiency is an inherited metabolic disorder that primarily affects children and adolescents. Since a lack of this enzyme causes elevated cholesterol levels, patients may need to pay special attention to their diet and lifestyle. The following are some suitable lifestyles for people with Ischemic deficiency:

1. Diet: reduce the intake of saturated fatty acids, increase unsaturated fatty acids, and the intake of cholesterol in food should be less than 300 mg/dl . It is recommended to increase plant-based foods such as vegetables, fruits, whole grains, beans, nuts and seeds, while reducing or avoiding high-cholesterol foods such as beef liver, pork liver, etc.

2. Exercise: Proper exercise is good for your health and can lower cholesterol levels. It is recommended to do 150 minutes of aerobic exercise per week, such as brisk walking, cycling or jogging.

3. Sleep: Ensuring adequate sleep time will help maintain good health. It is recommended to get 7-9 hours of sleep every night, and try to fall asleep before 10 pm.

4. Reduce stress: Moderate stress can improve emotional and mental health, but long-term excessive stress can lead to physical discomfort. Therefore, you should learn to cope with stress, including relaxation techniques such as meditation, yoga, deep breathing, etc.

5. Supplements: Based on your doctor's advice, you may need to take supplements such as vitamins A, D, E, K, and coenzyme Q10. In short, people with Ischemic deficiency need to pay attention to diet, exercise, sleep and reduce stress. Under the guidance of a doctor, proper supplementation may help improve physical health.

Other Diseases

Phosphoglycerate Dehydrogenase Deficiency Pyruvate Dehydrogenase Deficiency 3-Hydroxyacyl-CoA Dehydrogenase Deficiency Succinic Semialdehyde Dehydrogenase Deficiency 17-Beta-Hydroxysteroid Dehydrogenase X Deficiency Fatty Aldehyde Dehydrogenase Deficiency Medium-Chain Acyl-CoA Dehydrogenase Deficiency Short-Chain Acyl-CoA Dehydrogenase Deficiency Very Long-Chain Acyl-CoA Dehydrogenase Deficiency Long-Chain 3-Hydroxyacyl-Coenzyme A Dehydrogenase Deficiency

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