About 3-Hydroxyacyl-CoA Dehydrogenase Deficiency

3-Hydroxyacyl-Coa Dehydrogenase Deficiency, also known as hadh deficiency, is related to long-chain 3-hydroxyacyl-coa dehydrogenase deficiency and hyperinsulinemic hypoglycemia, familial, 4, and has symptoms including emaciation An important gene associated with 3-Hydroxyacyl-Coa Dehydrogenase Deficiency is HADH (Hydroxyacyl-CoA Dehydrogenase). The drugs Naloxone and Buprenorphine have been mentioned in the context of this disorder. Affiliated tissues include liver, heart and skeletal muscle, and related phenotypes are feeding difficulties in infancy and growth delay

Major Symptoms of 3-Hydroxyacyl-CoA Dehydrogenase Deficiency

3-hydroxyacyl-CoA dehydrogenase (3-HAC) deficiency is a rare genetic disorder characterized by the inability to convert 3-hydroxyacyl-CoA (3-HAC) to 3-methylbutyrate, a key step in the citric acid cycle. The major symptoms of 3-HAC deficiency include:

Suitable Lifestyle for People with 3-Hydroxyacyl-CoA Dehydrogenase Deficiency

3-hydroxyacyl-CoA dehydrogenase (3-HAC) deficiency is a rare genetic disorder that affects the metabolism of fatty acids, leading to a range of health problems. In terms of lifestyle, patients with 3-HAC deficiency should follow a specific diet to meet their unique nutritional needs. The dietary recommendations for patients with 3-HAC deficiency vary depending on the severity of the condition and individual tolerance. However, in general, they should avoid or limit the intake of fatty or high-fat foods, such as meat, dairy products, and fatty fish. Instead, they should focus on a low-fat, plant-based diet that includes a variety of fruits, vegetables, whole grains, and lean protein sources. It is important to consult with a healthcare professional or a registered dietitian who specializes in nutrition to develop a personalized meal plan that meets the specific needs of each patient. Additionally, patients with 3-HAC deficiency may require specialized dietary supplements or supplements to help meet their nutritional requirements. In summary, patients with 3-HAC deficiency should follow a low-fat, plant-based diet that is tailored to their unique nutritional needs. They should consult with a healthcare professional or a registered dietitian who specializes in nutrition to develop a personalized meal plan that meets their specific requirements.

Other Diseases

Long-Chain 3-Hydroxyacyl-Coenzyme A Dehydrogenase Deficiency Pyruvate Dehydrogenase Deficiency Isobutyryl-CoA Dehydrogenase Deficiency Phosphoglycerate Dehydrogenase Deficiency Fatty Aldehyde Dehydrogenase Deficiency Succinic Semialdehyde Dehydrogenase Deficiency 17-Beta-Hydroxysteroid Dehydrogenase X Deficiency Short-Chain Acyl-CoA Dehydrogenase Deficiency Medium-Chain Acyl-CoA Dehydrogenase Deficiency Very Long-Chain Acyl-CoA Dehydrogenase Deficiency

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