About Progressive Familial Intrahepatic Cholestasis

Cholestasis, Progressive Familial Intrahepatic, 1, also known as byler disease, is related to cholestasis, progressive familial intrahepatic, 3 and cholestasis, progressive familial intrahepatic, 4, and has symptoms including diarrhea, icterus and pruritus. An important gene associated with Cholestasis, Progressive Familial Intrahepatic, 1 is ATP8B1 (ATPase Phospholipid Transporting 8B1), and among its related pathways/superpathways are Transport of inorganic cations/anions and amino acids/oligopeptides and Cardiac conduction. The drugs Bile Acids and Salts and Liver Extracts have been mentioned in the context of this disorder. Affiliated tissues include liver, appendix and lung, and related phenotypes are osteopenia and hepatomegaly

Major Symptoms of Progressive Familial Intrahepatic Cholestasis

Progressive familial intrahepatic cholestasis (PFIC) is a rare genetic liver disease that can cause progressive liver damage due to inflammation. Some of the major symptoms of PFIC include jaundice, itching, dark urine, and abdominal pain. Additionally, people with PFIC may experience fatigue, loss of appetite, and a low white blood cell count.

Suitable Lifestyle for People with Progressive Familial Intrahepatic Cholestasis

Suitable lifestyles for people with Progressive familial intrahepatic cholestasis (PFIC) include the following:

1. Healthy diet: PFIC patients need to control the intake of fat and cholesterol in the diet, while increasing the intake of vegetables, fruits and whole grains . It is recommended to reduce high-fat and high-cholesterol foods, such as fried foods, cakes, chocolate, fish, shrimp, etc. , and increase low-fat and low-cholesterol foods, such as lean meat, chicken, turkey, beans, whole-wheat bread, and brown rice. wait.

2. Avoid drinking alcohol and smoking: PFIC patients should avoid drinking alcohol and smoking, as these habits can have a negative impact on the liver and aggravate the symptoms of PFIC.

3. Regular exercise: Moderate aerobic exercise can improve the body's metabolic level and relieve the symptoms of PFIC. It is recommended to perform at least 150 minutes of aerobic exercise per week, such as walking, jogging, swimming, etc.

4. Weight control: PFIC patients need to control their weight to reduce the burden on the liver. It is recommended to measure your weight at least 1-2 times a week and take corresponding weight loss measures as needed.

5. Follow your doctor's treatment recommendations: PFIC is a genetic disease that usually requires a doctor's treatment recommendations. Patients should follow their doctor's treatment plan, including medication, dietary adjustments, and necessary surgeries. PFIC patients need to control their diet, avoid bad lifestyle habits, engage in moderate exercise, control their weight, and follow doctors' treatment recommendations to improve symptoms, delay disease progression, and promote recovery to health.

Other Diseases

Progressive Familial Intrahepatic Cholestasis Type 1 Progressive Familial Intrahepatic Cholestasis Type 3 Progressive Familial Intrahepatic Cholestasis Type 2 Intrahepatic Cholestasis Benign Recurrent Intrahepatic Cholestasis 1 Gaze Palsy, Familial Horizontal, with Progressive Scoliosis, 2 Cholestasis Intrahepatic Cholecystolithiasis Primary Progressive Aphasia Progressive Myoclonic Epilepsy

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